Definition:
Pachydermoperiostosis is categorized as a rare disorder that is primarily characterized by clubbing of the fingers, excessive sweating and thickening of the skin of the face. It medical condition typically appears during early childhood or adolescence, and progresses slowly within the next ten year or so.
Diagnosis:
This disease is diagnosed using radiographs conducted on the long bones, which may reveal some subperiosteal new bone formation. Other radiographic abnormalities can also include cortical thickening and paranasal sinuses.
Treatment:
Treatment are primarily administered to alleviate this medical condition. Cortisteroids and Nonsteroidal anti-inflammatory drugs are among the common medications. Surgery may also be required in severe cases in the form of a vagotomy that is designed to improve swelling and articular pain. Other patients may also undergo cosmetic surgery.
Symptoms and Signs:
Specific symptoms of Pachydermoperiostosis include the enlargement of the patient’s fingers and toes. This condition features fibrous covering present on the ends of the long bones, and often accompanied with coarse facial features as well as an increased mass of the skin development on the scalp that results to the formation of folds, furrows and depressions.
Causes:
PDP is often considered as familial in nature, which means it is an inherited condition believed to be autonomic dominant. PDP can also be brought about by other underlying medical conditions such as myelofibrosis, compressive neuropathy, psoriatric onychopathy and gynecomastia as well as congenital cardiac disease.
The information on this site is for research purposes only and can not substitute for the advice of a medical professional. Ailments.com is not run by doctors and does not engage in the practice of medicine. Our site is not a medical authority, it is just a research tool for you to use in preparation for consulting with a doctor. We can not guarantee our information is accurate or up to date. Even if a statement made about a medical condition is accurate, it may not apply to you or your symptoms, so you should always consult a doctor. Nothing on our site should be construed as an attempt to offer or render a medical opinion or otherwise engage in the practice of medicine.
