Bannayan-Zonana syndrome or other term is Bannayan-Riley-Ruvalcaba syndrome is an unusual hamartomatous disorder through the incidence of several subcutaneous macrocephaly, lipomas and hemangiomas. In an autosomal prevailing form the disease is inherited though wild cases have been documented. Hamartomatous polyposis syndrome is the family where the disease belongs that also involves juvenile polyposis, Peutz-Jeghers syndrome and Cowden syndrome. BZS lesions are slowly developing and simply resectable. Intracranial association and visceral may happen in unusual conditions and can result to bleeding and indicative automatic compression particularly of the spinal cord or spinal nerve roots and may need surgical resection.

Bannayan-Zonana syndrome is categorized as a “rare disease” according to the Office of Rare Diseases (ORD) of the National Institutes of Health (NIH). This indicates that Bannayan-Zonana syndrome or a subtype of Bannayan-Zonana syndrome affects not more than 200,000 individuals in the US population.

Complications include intussusception and rectal bleeding. Other terms and pseudonym Primary name of the disease: Bannayan-Zonana syndrome Other terms or spellings for Bannayan-Zonana syndrome are as follows: Ruvalcaba -Myhre-Smith syndrome, Macrocephaly, Riley-Smith syndrome, Multiple lipomas, Hemangiomata, Bannayan-Riley-Ruvalcaba syndrome, Macrocephaly, pseudopapilledema and multiple hemangiomas, BZS, BRRS, RMSS, Ruvalcaba-Myhre syndrome, Bannayan syndrome, Macrocephaly-hamartomas syndrome, Macrocephaly-multiple lipomas-hemangiomata syndrome and Macrocephaly-pseudoepithelioma-multiple hemangiomas syndrome.

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